Syndromes/Craniofacial Anomalies
Benjamin A. Olson, DDS
Pediatric Dental Resident
Children's Mercy Hospital Kansas City
Children's Mercy Hospital Kansas City
Riverside, Missouri, United States
Brenda Bohaty, DDS
Program Director
Children's Mercy Kansas City
Kansas City, Missouri, United States
Solitary Median Maxillary Incisor and Holoprosencephaly: A review of the literature and report of a case.
Case Presentation Abstract
A solitary median maxillary incisor (SMMCI) is a rare anomaly that affects approximately 1:50,000 live births. The presence of an SMMCI tooth may be an isolated finding or may be associated with other anomalies such as Holoprosencephaly. Early recognition of SMMCIS is important given the possibility of other associated findings that may impact pediatric growth and development. The purpose of this report is to report the clinical findings associated with a one-year-old patient who presented to the clinic with a primary solitary median maxillary incisor and a diagnosis of Holoprosencephaly. This presentation will review the literature regarding the medical and dental findings associated with Holoprosencephaly and will discuss strategies for appropriately diagnosing and managing care for such patients.