527 - Ectodermal Dysplasia: A Family Tree

Ectodermal Dysplasia: A Family Tree

Potee EA, Ferretti GA, Ferretti ME, An Y

Department of Pediatric Dentistry; Rainbow Babies and Children’s Hospital

Case Western Reserve University School of Dental Medicine, Cleveland, OH.

Ectodermal dysplasia (ED) consists of a large group of inherited disorders in which two or more of the ectodermally-derived structures such as the skin, sweat glands, hair, nails, and teeth develop abnormally.

Especially important in pediatric dentistry are the distinguishing oral characteristics including hypodontia, hypoplastic conical teeth, and underdeveloped alveolar ridges. Due to children afflicted with ED often having low self-esteem, treatment goals should be aimed at creating a normal dental appearance. This presentation discusses three siblings with an autosomal dominant form of ectodermal dysplasia. All siblings are currently followed by the craniofacial clinic at Case Western Reserve University. This poster will evaluate and compare the panoramic films of each sibling, with a focus on the youngest sibling who has undergone dental treatment in the OR under general anesthesia for treatment of dental caries using esthetic restorations.