495 - Management of Patient with Epidermolysis Bullosa: A Case Report

This case report discusses the presentation, oral manifestations, and management of dental diseases for pediatric patients with Epidermolysis Bullosa (EB). Epidermolysis bullosa is a genetic disorder characterized by blistering, erosions, and scar formation of the skin and mucosa following mechanical trauma. There are four major types of EB that differ phenotypically and genotypically with oral manifestations. Oral care and maintenance of these children are challenging as they need a vigorous caries management plan guided by risk assessment at home and dental office as well as staged restorative and surgical intervention in dental office and under general anesthesia. This report discusses dental management of an 18-year-old male patient with recessive dystrophic epidermolysis bullosa at UCSF Pediatric Dentistry clinic since 2011. This case reports highlights the prevention and management of oral diseases in children with EB with an emphasis on soft tissue management and anesthesia.