411 - Case Report of Solitary Median Maxillary Central Incisor Syndrome

Introduction: Solitary Median Maxillary Central Incisor (SMMCI) syndrome is a rare midline disorder of hypodontia resulting from a developmental deficiency in utero and is associated with several other craniofacial midline anomalies. Medical management of associated findings requires multispecialty collaboration, including management of the solitary incisor. Treatment of the single tooth may include restorative, orthodontic, or prosthodontic care. Alternatively, the tooth can be left untreated as it is primarily an esthetic concern.

Case Report: A 13-month old female with a history of congenital nasal pyriform aperture stenosis presented to Children’s Wisconsin dental clinic after being referred by ENT. Due to young age, extent of treatment needs, and coordination with ENT for additional treatment needs, patient was evaluated and planned for dental treatment in the OR. The parent was presented several treatment options for tooth #E: single anterior strip crown, prefabricated porcelain-faced crown, facial resin shaped and contoured to appear as 2 central incisors. The parent elected to attempt the single anterior strip crown restoration.