Patient Management
Maria T. Rodriguez, DMD
Pediatric Dentistry Resident
University of Puerto Rico School of Dental Medicine
University of Puerto Rico School of Dental Medicine
GUAYNABO, Puerto Rico, United States
Rosana Hanke, DMD, MSD
University of Puerto Rico School of Dental Medicine
Emilio Agrait, DMD
Program Director Advanced Education Program in Pediatric Dentistry
University of Puerto Rico School of Dental Medicine
San Juan, Puerto Rico, United States
Introduction: Ectodermal Dysplasia is a genetic disorder that affects 7 per 10,000 births. This condition disrupts development of at least two structures derived from the ectoderm. Thus, tissues such as skin, hair follicles, sebaceous glands, and teeth may be abnormal in individuals with the condition. Oral manifestations include oligodontia, dental hypoplasia or conical shaped teeth. Ectodermal Dysplasia affects dental form, function and has significant psychosocial implications for patients.
Case Report: This presentation discusses a 9 year old male patient who presented to University of Puerto Rico School of Dental Medicine with a chief complaint of bullying associated to his dental condition. Clinical and radiographic examinations revealed oligodontia, excessive overjet and dental caries. Restorative and preventive oral interventions were performed followed by interceptive orthodontic and prosthetic treatment. This case report details the clinical and radiographic findings associated with Ectodermal Dysplasia as well as the complete oral rehabilitation rendered to our patient.